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Frontiers of Medicine >> 2019, Volume 13, Issue 2 doi: 10.1007/s11684-018-0634-z
Clinical characteristics in lymphangioleiomyomatosis-related pulmonary hypertension: an observation on 50 patients
. Department of Respiratory Medicine, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing 100730, China;.. Department of Cardiology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing 100730, China
Abstract
Keywords
lymphangioleiomyomatosis ; pulmonary hypertension ; pulmonary function ; hypoxemia ; sirolimus
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