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2019 1

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hypoxemia 1

lymphangioleiomyomatosis 1

pulmonary function 1

pulmonary hypertension 1

sirolimus 1

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Clinical characteristics in lymphangioleiomyomatosis-related pulmonary hypertension: an observation on 50 patients

Xiuxiu Wu, Wenshuai Xu, Jun Wang, Xinlun Tian, Zhuang Tian, Kaifeng Xu

Frontiers of Medicine 2019, Volume 13, Issue 2,   Pages 259-266 doi: 10.1007/s11684-018-0634-z

Abstract: characteristics of LAM with elevated pulmonary artery pressure (PAP) and evaluate the potential efficacy of sirolimusMoreover, in 10 patients who received sirolimus therapy, SPAP decreased from 57.0±12.6 mmHg to 35.2±11.1showed that LAM patients with PH exhibit poor pulmonary function and hypoxemia and may benefit from sirolimus

Keywords: lymphangioleiomyomatosis     pulmonary hypertension     pulmonary function     hypoxemia     sirolimus    

Title Author Date Type Operation

Clinical characteristics in lymphangioleiomyomatosis-related pulmonary hypertension: an observation on 50 patients

Xiuxiu Wu, Wenshuai Xu, Jun Wang, Xinlun Tian, Zhuang Tian, Kaifeng Xu

Journal Article